From: 10th Congress of International Society of Systemic Auto-Inflammatory Diseases (ISSAID)
Characteristics | HA20 | BD | p | Odds ratio | 95%CI | |||
---|---|---|---|---|---|---|---|---|
(n=54) | (%) | (n=520) | (%) | |||||
Age at onset (years) (mean ± SD) | 6.1 ± 6.5 |  | 36.4 ± 12.3 |  | < 0.001 | 533.71 | 171.84 | 1657.65 |
Familial history | 15 /25 | 60 | 19 /332 | 5.7 | < 0.001 | 24.71 | 9.8 | 62.29 |
Recurrent fever | 37 /50 | 74 | 39 /364 | 10.7 | < 0.001 | 23.72 | 11.62 | 48.43 |
Oral ulcer | 46 /52 | 88.5 | 518 /520 | 99.6 | < 0.001 | 0.03 | 0.01 | 0.15 |
Genital ulcer | 34 /52 | 65.4 | 372 /520 | 71.5 | 0.35 | 0.75 | 0.41 | 1.37 |
Eye involvement | 5 /51 | 9.8 | 330 /520 | 63.5 | < 0.001 | 0.06 | 0.02 | 0.16 |
Skin involvement | 27 /51 | 52.9 | 461 /520 | 88.7 | < 0.001 | 0.14 | 0.08 | 0.27 |
Gastrointestinal involvement | 22 /52 | 40.7 | 78 /520 | 15 | < 0.001 | 4.16 | 2.28 | 7.58 |