From: Health-related quality of life in children with inflammatory brain disease
Female. Number (%) | 80 (55%) |
Age at diagnosis, years. Median (range) | 10.3 (0.4–18.2) |
Diagnosis | |
Small vessel cPACNS | 48 (33%) |
Angiography positive, non-progressive cPACNS | 22 (15%) |
Angiography positive, progressive cPACNS | 8 (6%) |
Antibody-mediated IBrainD | 26 (18%) |
Anti-NMDA receptor encephalitis | 13 (9%) |
Other antibody-mediated | 13 (9%) |
Secondary IBrainD | 12 (8%) |
Secondary CNS Vasculitis | 10 (7%) |
Demyelinating | 4 (3%) |
Granulomatosis IBrainD | 2 (1%) |
Moyamoya-like | 1 (1%) |
T-cell mediated IBrainD | 2 (1%) |
IBrainD NYD | 10 (7%) |
Time to diagnosis, months. Median (range) | 1.2 (0–150) |