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Table 1 Patient demographics for 145 pediatric patients with inflammatory brain disease

From: Health-related quality of life in children with inflammatory brain disease

Female. Number (%)

80 (55%)

Age at diagnosis, years. Median (range)

10.3 (0.4–18.2)

Diagnosis

 

 Small vessel cPACNS

48 (33%)

 Angiography positive, non-progressive cPACNS

22 (15%)

 Angiography positive, progressive cPACNS

8 (6%)

 Antibody-mediated IBrainD

26 (18%)

  Anti-NMDA receptor encephalitis

13 (9%)

  Other antibody-mediated

13 (9%)

 Secondary IBrainD

12 (8%)

 Secondary CNS Vasculitis

10 (7%)

 Demyelinating

4 (3%)

 Granulomatosis IBrainD

2 (1%)

 Moyamoya-like

1 (1%)

 T-cell mediated IBrainD

2 (1%)

 IBrainD NYD

10 (7%)

Time to diagnosis, months. Median (range)

1.2 (0–150)

  1. Legend: Acronyms: CNS Central nervous system, cPACNS Childhood primary angiitis of the central nervous system, IBrainD Inflammatory brain disease, NYD Not yet determined