Age at diagnosis (median;IQR years)
| |
10.7 (8.9 to 12.7)
|
Gender F/M;ratio
| |
94/37;2.54
|
Clinical Characteristics
|
Bone pain (n = 129)
|
118 (91.4%)
|
Swelling (n = 102)
|
50 (49.01%)
|
Fever (n = 79)
|
6 (7.59%)
|
Symmetrical symptoms (n = 125)
|
24 (19.2%)
|
Clinical unifocal involvement
|
92 (70.22%)
|
Synovitis
|
9 (6.87%)
|
Arthritis
|
9 (6.87%)
|
Hyperostosis
|
43 (32.82%)
|
Number of sites
|
Clinical
|
1.29 (range 0–3)
|
Radiological
|
3.27 (range 1–13)
|
Extraosseous involvement
|
Psoriasis
|
5 (3.87%)
|
Ulcerative colitis
|
1 (0.76%)
|
Pustulosis
|
10 (7.63%)
|
Investigations
|
Raised inflammatory markers (n = 126)
|
50 (39.68%)
|
ANA positive (n = 26)
|
3 (11.53%)
|
HLA B27 positive (n = 15)
|
1 (6.66%)
|
Bone biopsy performed
|
73 (55.72%)
|
Positive culture (n = 3) from bone biopsy
|
Coagulase negative staphylococcus: 2 (66.66%)
|
Staphylococcus aureus: 1 (33.33%)
|
Family history of-
|
Psoriasis (n = 130)
|
20 (15.38%)
|
Inflammatory bowel disease (n = 130)
|
4 (3.07%)
|
Autoimmune disorders (n = 130)
|
6 (4.61%)
|