Patient # | 1 | 2 | 3 | 4 | 5 | 6 | 7 | 8 |
---|---|---|---|---|---|---|---|---|
Age at diagnosis | 2Â months | 16Â years | 8Â years | 5Â years | 14Â years | 8Â years | 5Â years | 13Â years |
Sex | Male | Male | Male | Female | Male | Male | Female | Female |
Ethnicity | Caucasian | Caucasian | Caucasian | Caucasian | Caucasian | Caucasian | Hispanic | Caucasian |
Palpable purpura | Yes | Yes | Yes | Yes | Yes | Yes | Yes | Yes |
Hematuria and/or proteinuria | Yes | Yes | Yes | Yes | Yes | Yes | Yes | Yes |
Renal biopsy pathology | Not done | WHO Class I | WHO Class III | WHO Class III | WHO Class III/IV | WHO Class II | WHO Class II | Not done |
Arthritis | No | No | Yes | No | No | No | No | Yes |
GI bleed/distress | No | Yes | Yes | Yes | Yes | Yes | Yes | Yes |
Long term CS use | Yes | Yes | No | Yes | Yes | Yes | Yes | Yes |
Immuno-modulators (Months of DMARD prior to 1st RTX) | MTX [1] | AZA [4] | CTX (1 dose) | None | MTX [2]; MMF (post); IVIG (post) | MTX (> 3 years intermittent) |