From: Towards a new set of classification criteria for PFAPA syndrome
Characteristic | |
---|---|
M/F | 1.2 |
Age at onset (years) | Median 1.9 (IQR 0.8–3.1) |
Age at diagnosis (years) | Median 4 (IQR 2.6–6) |
Pharyngitis | 88.7% |
Adenitis | 85.0% |
Aphthous Stomatitis | 71.2% |
Headaches | 30.0% |
Digestive: | |
• Nausea | 6.25% |
• Vomiting | 20.0% |
• Abdominal pain | 48.7% |
• Diarrhea | 22.5% |
• Hepatomegaly | 1.2% |
• Splenomegaly | 7.5% |
Arthralgia | 33.7% |
Arthritis | 1.2% |
General malaise | 37.5% |
Skin rash | 21.2% |
Conjunctivitis | 8.7% |
Myalgia | 26.2% |
Neurological symptoms (febrile seizure, one encephalitis) | 5% |
Acute scrotum | 1.2% |
Peritonitis | 0% |