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Table 3 Characteristics of 80 PFAPA patients included in the analysis

From: Towards a new set of classification criteria for PFAPA syndrome

Characteristic

 

M/F

1.2

Age at onset (years)

Median 1.9 (IQR 0.8–3.1)

Age at diagnosis (years)

Median 4 (IQR 2.6–6)

Pharyngitis

88.7%

Adenitis

85.0%

Aphthous Stomatitis

71.2%

Headaches

30.0%

Digestive:

• Nausea

6.25%

• Vomiting

20.0%

• Abdominal pain

48.7%

• Diarrhea

22.5%

• Hepatomegaly

1.2%

• Splenomegaly

7.5%

Arthralgia

33.7%

Arthritis

1.2%

General malaise

37.5%

Skin rash

21.2%

Conjunctivitis

8.7%

Myalgia

26.2%

Neurological symptoms (febrile seizure, one encephalitis)

5%

Acute scrotum

1.2%

Peritonitis

0%