Skip to main content

Table 3 Characteristics of 80 PFAPA patients included in the analysis

From: Towards a new set of classification criteria for PFAPA syndrome

Characteristic  
M/F 1.2
Age at onset (years) Median 1.9 (IQR 0.8–3.1)
Age at diagnosis (years) Median 4 (IQR 2.6–6)
Pharyngitis 88.7%
Adenitis 85.0%
Aphthous Stomatitis 71.2%
Headaches 30.0%
Digestive:
• Nausea 6.25%
• Vomiting 20.0%
• Abdominal pain 48.7%
• Diarrhea 22.5%
• Hepatomegaly 1.2%
• Splenomegaly 7.5%
Arthralgia 33.7%
Arthritis 1.2%
General malaise 37.5%
Skin rash 21.2%
Conjunctivitis 8.7%
Myalgia 26.2%
Neurological symptoms (febrile seizure, one encephalitis) 5%
Acute scrotum 1.2%
Peritonitis 0%