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Table 1 Categories and variables reaching consensus during both Delphi

From: Towards a new set of classification criteria for PFAPA syndrome

Categories/variables

Consensus (80%)

1. Recurrent fever attacks

Delphi 1

 Duration of attacks

no

 Regularity of fever attacks

no

2. Constitutional symptoms

Delphi 1

 Actual criteriona

no

 New criterionb

Delphi 2

3. Exclusion

Delphi 1

 Exclusion of autoinflammatory diseases

Delphi 2

 Exclusion of infections and related conditions

Delphi 2

4. Age limitation for onset

no

5. Well-being between episodes

Delphi 2

6. Growth and development

Delphi 2

7. Response to steroid treatment

Delphi 2

8. Other

no

  1. aPhrased as in Marshall’s criteria; bmodify Marshall’s criteria