From: Towards a new set of classification criteria for PFAPA syndrome
Categories/variables | Consensus (80%) |
---|---|
1. Recurrent fever attacks | Delphi 1 |
Duration of attacks | no |
Regularity of fever attacks | no |
2. Constitutional symptoms | Delphi 1 |
Actual criteriona | no |
New criterionb | Delphi 2 |
3. Exclusion | Delphi 1 |
Exclusion of autoinflammatory diseases | Delphi 2 |
Exclusion of infections and related conditions | Delphi 2 |
4. Age limitation for onset | no |
5. Well-being between episodes | Delphi 2 |
6. Growth and development | Delphi 2 |
7. Response to steroid treatment | Delphi 2 |
8. Other | no |