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Table 1 (abstract 175). Demographical data and evolution of different disease groups

From: Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)

  CAPS TRAPS MKD FMF BEHCET CRMO SAPHO All patients
Number of patients (families) 21
(19)
5
(5)
16
(15)
38
(34)
20
(20)
61
(61)
5
(5)
166
(159)
Gender (M;F) 8;13 1;4 5;11 16;22 12;8 18;43 2;3 62;104
Age at disease onset* (years) 0†
(0†-11)
5,5
(0-11)
1
(0†-11)
3
(0-9)
6
(0-12)
9.5
(3-14)
8
(4-15)
8
(0-15)
Duration of follow-up* (years) 7
(0,5-26)
3,75
(0-9)
4,25
(0-18)
3,5
(1-18)
2,75
(0-16)
12.5
(0-17)
2
(0-2,5)
8
(0-26)
Complications or side effects (%) 15
(71)
3
(60)
9
(56)
9
(23)
15
(75)
15
(24)
1
(20)
67
(40)
Number of biologic DMRADs* 2
(1-3)
1
(1-1)
2
(0-4)
0
(0-2)
0
(0-2)
0
(0-1)
0
(0-0)
0
(0-4)
Clinical remission on treatment (%) 18
(85)
0
(0)
9
(56)
24
(63)
7
(35)
15
(24)
0
(0)
73
(44)
Clinical remission off treatment (%) 0
(0)
1
(20)
0
(0)
2
(5)
0
(0)
13
(21)
3
(60)
19
(11.5)
Relapse after remissions (%) 2
(9)
1
(20)
3
(18)
1
(2)
0
(0)
7
(11)
0
(0)
14
(8)
  1. *median (range); † day 1 of life