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Table 1 (abstract 175). Demographical data and evolution of different disease groups

From: Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)

  CAPS TRAPS MKD FMF BEHCET CRMO SAPHO All patients
Number of patients (families) 21 (19) 5 (5) 16 (15) 38 (34) 20 (20) 61 (61) 5 (5) 166 (159)
Gender (M;F) 8;13 1;4 5;11 16;22 12;8 18;43 2;3 62;104
Age at disease onset* (years) 0† (0†-11) 5,5 (0-11) 1 (0†-11) 3 (0-9) 6 (0-12) 9.5 (3-14) 8 (4-15) 8 (0-15)
Duration of follow-up* (years) 7 (0,5-26) 3,75 (0-9) 4,25 (0-18) 3,5 (1-18) 2,75 (0-16) 12.5 (0-17) 2 (0-2,5) 8 (0-26)
Complications or side effects (%) 15 (71) 3 (60) 9 (56) 9 (23) 15 (75) 15 (24) 1 (20) 67 (40)
Number of biologic DMRADs* 2 (1-3) 1 (1-1) 2 (0-4) 0 (0-2) 0 (0-2) 0 (0-1) 0 (0-0) 0 (0-4)
Clinical remission on treatment (%) 18 (85) 0 (0) 9 (56) 24 (63) 7 (35) 15 (24) 0 (0) 73 (44)
Clinical remission off treatment (%) 0 (0) 1 (20) 0 (0) 2 (5) 0 (0) 13 (21) 3 (60) 19 (11.5)
Relapse after remissions (%) 2 (9) 1 (20) 3 (18) 1 (2) 0 (0) 7 (11) 0 (0) 14 (8)
  1. *median (range); † day 1 of life