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Table 1 (abstract P170). Demographic features of enrolled patients

From: Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)

Disease Pts number M/F Mean onset age (years, range) Mean diagnosis age (years, range) Western Europe Eastern Europe Eastern- Southern Mediterranean Others Countries
Monogenic Disease
 FMF 1078 561/517 6 (0-66) 10 (0-72) 540 120 290 128
 CAPS 296 145/151 5 (0-57) 19 (0-77) 239 27 13 17
 TRAPS 271 138/133 9 (0-63) 21 (0-77) 238 25 4 4
 MKD 204 92/112 2 (0-45) 12 (0-51) 175 17 5 7
 Blau disease 49 25/24 3 (0-29) 8 (0-45) 24 1 3 21
 PAPA 40 20/20 6 (0-18) 19 (2-57) 31 5 2 2
 DADA2 13 10/3 4 (0-10) 12 (6-18) 10 - 3 -
 NLRP-12 12 6/6 12(0-29) 37 (4-76) 11 - - 1
 SAVI 3 1/2 1 (0-4) 10 (1-17) 2 - - 1
 DIRA 3 0/3 1mth 2 (0-7) 2 - 1 -
 Majeed 3 3/0 18 (0-55) 23 (1-68) 3 - - -
 CANDLE 1 0/1 10 12 1 - - -
Multifactorial autoinflammatory disease
 PFAPA 664 376/288 2 (0-29) 5 (0-37) 333 224 94 13
 CNO 564 210/354 11 (0-62) 12 (1-68) 513 16 24 11
 Undefined fever 346 170/176 12 (0-73) 17 (0-75) 295 40 4 7
 Behcet 214 108/106 9 (0-56) 12 (2-57) 189 14 9 2
 Schnitzler 12 5/7 53 (36-75) 57 (41-78) 12 - - -
Total 3773 1870/1903 - - 2618 489 452 214