Table 1 (abstract P170). Demographic features of enrolled patients
From: Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)
Disease | Pts number | M/F | Mean onset age (years, range) | Mean diagnosis age (years, range) | Western Europe | Eastern Europe | Eastern- Southern Mediterranean | Others Countries |
|---|---|---|---|---|---|---|---|---|
Monogenic Disease | ||||||||
 FMF | 1078 | 561/517 | 6 (0-66) | 10 (0-72) | 540 | 120 | 290 | 128 |
 CAPS | 296 | 145/151 | 5 (0-57) | 19 (0-77) | 239 | 27 | 13 | 17 |
 TRAPS | 271 | 138/133 | 9 (0-63) | 21 (0-77) | 238 | 25 | 4 | 4 |
 MKD | 204 | 92/112 | 2 (0-45) | 12 (0-51) | 175 | 17 | 5 | 7 |
 Blau disease | 49 | 25/24 | 3 (0-29) | 8 (0-45) | 24 | 1 | 3 | 21 |
 PAPA | 40 | 20/20 | 6 (0-18) | 19 (2-57) | 31 | 5 | 2 | 2 |
 DADA2 | 13 | 10/3 | 4 (0-10) | 12 (6-18) | 10 | - | 3 | - |
 NLRP-12 | 12 | 6/6 | 12(0-29) | 37 (4-76) | 11 | - | - | 1 |
 SAVI | 3 | 1/2 | 1 (0-4) | 10 (1-17) | 2 | - | - | 1 |
 DIRA | 3 | 0/3 | 1mth | 2 (0-7) | 2 | - | 1 | - |
 Majeed | 3 | 3/0 | 18 (0-55) | 23 (1-68) | 3 | - | - | - |
 CANDLE | 1 | 0/1 | 10 | 12 | 1 | - | - | - |
Multifactorial autoinflammatory disease | ||||||||
 PFAPA | 664 | 376/288 | 2 (0-29) | 5 (0-37) | 333 | 224 | 94 | 13 |
 CNO | 564 | 210/354 | 11 (0-62) | 12 (1-68) | 513 | 16 | 24 | 11 |
 Undefined fever | 346 | 170/176 | 12 (0-73) | 17 (0-75) | 295 | 40 | 4 | 7 |
 Behcet | 214 | 108/106 | 9 (0-56) | 12 (2-57) | 189 | 14 | 9 | 2 |
 Schnitzler | 12 | 5/7 | 53 (36-75) | 57 (41-78) | 12 | - | - | - |
Total | 3773 | 1870/1903 | - | - | 2618 | 489 | 452 | 214 |