Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)

Table 1 (abstract P086). See text for description

Patient / Sex	1 / F	2 / F	3 / M	4 / F
Lung disease	Bronchiolitis Obliterans with Organizing Pneumonia	Surfactant Protein C-associated ILD	Non-specific interstitial pneumonia	Chronic bronchiectasis
Age at ILD onset (y)	16,9	2	14,4	10,9
Chest X-ray and scanner abnormalities	Yes	Yes	Yes	Yes
Diffusion trouble	Yes	Yes	Yes	No
Restrictive syndrome	No	No	No	No
Obctructive syndrome	No	Yes	No	No
Inflammatory alveolar liquid	No	Yes		No
Biologics	Ritux	Eta	Eta, Toci, Aba, Inflix	No
IV steroids	Yes	Yes	No	No

ISSN: 1546-0096