From: Proceedings of the 25th European Paediatric Rheumatology Congress (PReS 2018)
Female/male (n:168) | 87(51.8)/81 (48.2) |
Mean age at disease onset | 76.7±54.5 months (IQR: 28-118) |
Mean age at diagnosis | 79,7±54.5 months (IQR: 33-121) |
Mean delay of diagnosis | 3.9 ± 8.7 months (IQR:1-3) |
Clinicalfeatures, n (%) | |
 Typical fever | 160(95.2) |
 Typical rash | 99(59) |
 Lymphadenopathy | 45(26.8). |
 Hepatosplenomegaly | 70(41.7) |
 Arthritis/arthralgia | 143(85.1), 25(14.9) |
 Pericarditis, pleuritis | 12(7.1), 3(1.8) |