Test in all JM Patients (n=9) | ||||||||||
---|---|---|---|---|---|---|---|---|---|---|
 | *CHAQ SDI | *Pt/Parent Global | PROMIS SF Pt/Parent | *MDAS | *MD global | *CMAS | *MMT8 | STS | TUG | 6MWD |
Echogencity Pre | 0.30 | 0.30 | -0.21 | 0.38 | 0.45 | -0.52 | -0.84 | -0.17 | -0.43 | -0.36 |
Echogencity Post | 0.34 | 0.34 | -0.28 | 0.45 | 0.50 | -0.56 | -0.84 | -0.10 | -0.43 | -0.30 |
Muscle thickness Pre | 0.01 | 0.04 | 0.04 | 0.08 | -0.08 | 0.32 | -0.20 | -0.47 | 0.08 | 0.10 |
Muscle thickness Post | -0.02 | -0.01 | -0.19 | 0.19 | 0.11 | 0.25 | -0.19 | -0.54 | -0.10 | 0.28 |
Elastography Pre | 0.05 | 0.03 | -0.18 | 0.10 | 0.12 | -0.24 | 0.27 | -0.34 | 0.15 | -0.34 |
Elastography Post | 0.01 | -0.04 | 0.39 | 0.29 | 0.20 | -0.06 | 0.22 | -0.66 | 0.05 | -0.02 |
Power doppler Pre | 0.29 | 0.29 | -0.45 | 0.41 | 0.42 | -0.41 | -0.41 | 0.28 | -0.22 | 0.14 |
Power doppler Post | 0.00 | 0.00 | 0.00 | 0.33 | 0.40 | -0.13 | -0.78 | -0.09 | -0.78 | 0.00 |
CEUS Tp Pre | -0.47 | -0.51 | -0.20 | -0.10 | -0.06 | 0.17 | 0.57 | -0.05 | -0.22 | 0.57 |
CEUS Tp Post | -0.27 | -0.29 | -0.30 | -0.76 | -0.60 | 0.19 | 0.43 | 0.00 | 0.55 | 0.14 |
CEUS Ip Pre | -0.33 | -0.33 | 0.04 | 0.21 | 0.16 | 0.00 | 0.39 | 0.15 | -0.49 | -0.04 |
CEUS Ip Post | 0.09 | 0.09 | 0.27 | 0.71 | 0.70 | -0.09 | -0.09 | -0.29 | -0.68 | 0.03 |
CEUS AUC Pre | -0.15 | -0.15 | 0.10 | -0.36 | -0.29 | -0.11 | -0.11 | 0.33 | 0.16 | 0.07 |
CEUS AUC Post | -0.09 | -0.09 | -0.27 | -0.37 | -0.43 | -0.26 | 0.60 | 0.90 | 0.68 | -0.37 |