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Table 3 Systemic involvement and underline disease

From: Clinical study of children with cryofibrinogenemia: a retrospective study from a single center

Case No. 1 2 3 4 5 6 7 8 No. Abnormal/Total %
Skin biopsy (+) (−) ND ND (+) ND ND (−) 2/4 50
Renal involvement 3/8 37.5
 Proteinuria (−) (−) (−) (−) (+) (+) (−) (−) 2/8 25
 Hematuria (−) (−) (−) (+) (+) (+) (−) (−) 3/8 37.5
 Renal insufficiency (−) (−) (−) (−) (−) (−) (−) (+) 1/8 12.5
Arthritis (+) (+) (+) (+) (+) (+) (+) (+) 8/8 100
Thrombotic events (−) (−) (+) (+) (−) (+) (+) (+) 5/8 62.5
 Angiogram ND ND (+) (+) ND (+) ND (+) 4/4 100
Respiratory involvement
 Pulmonary embolism (+) ND (−) ND (−) ND (−) ND 1/4 25
 ARDS (+) (−) (+) (+) (−) (−) (+) (−) 4/8 50
Neurological involvement
 Multineuritis (+) (−) (+) ND (−) (−) (−) (+) 3/7 42.9
 Brain MRI (−) (−) (+) (+) ND (−) (+) (+) 4/7 57.1
 Spine MRI ND ND (−) ND ND ND ND (−) 0/2 0
 SSEP ND (−) (−) ND ND (−) ND ND 0/3 0
 EMG ND (−) ND ND ND ND (+) ND 1/2 50
 EEG ND (+) (−) ND ND ND (+) (+) 3/4 75
 BAEP ND (−) ND ND ND (−) (−) (+) 1/4 25
 VEP ND ND ND ND ND ND (+) (+) 2/2 100
Associated disease
 Autoimmune disease CG (−) JIA JIA JIA, JDM, SLE JIA B, SLE, JIA CM, JIA, B 6/8 75
 HCV/HBV infection (−) (−) (−) (−) (−) (−) (−) (−) 0 0
  1. (+) = abnormal; (−) = normal; ND = not done
  2. ARDS acute respiratory distress syndrome, NCV nerve conduction velocity, EMG electromyogram, SSEP somatosensory evoked potential, BAEP brainstem auditory evoked potential, VEP visual evoked potential, HCV hepatitis C virus infection, HBV hepatitis B virus infection, CG cryoglobulinemia, JIA juvenile idiopathic arthritis, JDM juvenile dermatomyositis, SLE systemic lupus erythematosus, B Behcet’s disease, CM Cutaneous mastocytosis