From: Clinical study of children with cryofibrinogenemia: a retrospective study from a single center
Case | 1 | 2 | 3 | 4 | 5 | 6 | 7 | 8 | No. Positive/No. All checked | (%) |
---|---|---|---|---|---|---|---|---|---|---|
Cryofibrinogen | (+) | (+) | (+) | (+) | (+) | (+) | (+) | (+) | 8/8 | (100) |
Cryoglobulin | (+) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |
α1-antitrypsin | ND | ND | (−) | ND | ND | (−) | ND | (−) | 0/3 | (0) |
PT/aPTT(initial) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |
Bleeding time | (−) | ND | ND | ND | ND | ND | ND | ND | 0/1 | (0) |
IgA | (−) | (−) | (−) | (−) | (−) | (−) | ND | (−) | 0/7 | (0) |
Platelet count | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/7 | (0) |
vWF | ND | (−) | I | (−) | (−) | I | (−) | (−) | 2/7 | (28.5) |
C3 | (−) | D | (−) | (−) | D | (−) | D | D | 4/8 | (50) |
C4 | (−) | (−) | (−) | D | (−) | D | I | D | 4/8 | (50) |
Protein C | I | (−) | (−) | I | I | (−) | I | I | 5/8 | (62.5) |
Protein S | I | (−) | D | D | D | D | D | I | 7/8 | (87.5) |
Anti-thrombin III | I | I | I | I | I | I | I | I | 8/8 | (100) |
Lupus anticoagulant | (−) | ND | (+) | (−) | (+) | (−) | (−) | (−) | 2/7 | (28.5) |
RA factor | (−) | (−) | (+) | (−) | (−) | (+) | (−) | (+) | 3/8 | (37.5) |
Antinuclear Factor | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (+) | 1/8 | (12.5) |
Anti-cardiolipin IgG | (−) | (−) | (−) | (−) | (+) | (−) | (−) | (−) | 1/8 | (12.5) |
Anti-cardiolipin IgM | (−) | (−) | (−) | (−) | (+) | (−) | (−) | (−) | 1/8 | (12.5) |
anti-ENA (all) | (−) | (−) | (−) | (−) | (+) | (−) | (−) | (−) | 1/8 | (12.5) |
Anti CCP | ND | ND | ND | (−) | (−) | (−) | (−) | (−) | 0/5 | (0) |
ANCA-C | (−) | (−) | ND | ND | (−) | (−) | (−) | (−) | 0/6 | (0) |
ANCA-P | (−) | (−) | ND | ND | (−) | (−) | (−) | (−) | 0/6 | (0) |
Anti-β2 GP1 IgG | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |
Anti-β2 GP1 IgM | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |
Anti-ds DNA | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |
Anti-SSA | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |
Anti-SSB | (−) | (−) | (−) | (−) | (−) | (−) | (−) | (−) | 0/8 | (0) |