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Fig. 3 | Pediatric Rheumatology

Fig. 3

From: Practice and consensus-based strategies in diagnosing and managing systemic juvenile idiopathic arthritis in Germany

Fig. 3

Treat-to-target consensus treatment strategy for definitive SJIA. Maximal doses for glucocorticoids: i.v. methylprednisolone pulse therapy (20–30 mg/kg/day [max. 1000 mg/day) for 5 days or prednisolone equivalent 1–2 mg/kg/day (max. 80 mg/day). “Biologic” refers to anakinra, canakinumab or tocilizumab. Maximal doses for biologics: anakinra 8 mg/kg/day (max. 300 mg/days), canakinumab 8 mg/kg (max. 600 mg) every 4 weeks, tocilizumab (for body weight > 30 kg) 8 mg/kg (max. 800 mg) i.v. every 2 weeks and (for body weight < 30 kg) 12 mg/kg every 2 weeks. In addition, non-steroidal anti-inflammatory drugs may be used for symptom relief throughout. Abbreviations: ANA, anakinra; CAN, canakinumab; CID, clinical inactive disease; GC, glucocorticoids; i.a., intraarticular; IVMP, intravenous methylprednisolone pulse; MTX, methotrexate; NSAID, nonsteroidal anti-inflammatory drug; PDN, prednisone/prednisolone equivalent; TCZ, tocilizumab; TNF, tumor necrosis factor-alpha. ↓ = decrease dose or frequency (taper); ↑ = increase dose or frequency

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