Fig. 2

Summary of treatment and clinical course for Case 1 (a), Case 2 (b) and Case 3 (c). Line chart of muscle strength (dotted line with circles, Manual muscle testing, MMT, range 0–80, low numbers indicate weakness) and creatine kinase (CK, intermittent line) from diagnosis. Bold arrows indicate treatment with Rituximab. Duration of treatment is represented by horizontal lines above chart. Short vertical lines indicate treatment with high dose intravenous methylprednisolone (IVMP). Narrowing of the top horizontal line represents tailing of the oral corticosteroid dose (PO prednisolone)