Table 1 Patient Characteristics for Skin Predominant Juvenile Dermatomyositis (JDM)

Patients Inclusion Characteristics

 1. Typical rash consistent with JDM for ≥6 weeks.

  a. Should include Gottron’s papules or heliotrope rash

  b. May have mild calcinosis and nailbed capillary abnormalities

 2. No functional limitations or weakness

  a. Based on history or CHAQ

  b. As determined by treating physician based on strength assessment

 3. Muscle enzymes ≤ 1.2 times upper limit of normal

  a. Except if attributed to another process, such as exercise or drug therapy

Patients Exclusion Characteristics

 1. Significant systemic involvement, including parenchymal lung disease, dysphagia, aspiration, intestinal vasculitis, myocarditis

 2. Significant calcinosis, as determined by treating clinician

 3. Ulcerative skin disease

 4. Lipodystrophy

 5. Pregnancy