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Table 4 Frequencies of clinical characteristics of BD in children compared to adults

From: Behçet’s disease in children, an overview

 

Paediatric series

Adult series

Clinical features in %

Karincaoglu [4]

Krause [37]

Koné- Paut [7]

Atmaca [35]

Koné-Paut + [13]

Alpsoy E [38]

Krause [37]

N = patients

33

19

65

110

156

661

34

Oral aphthosis

100

100

96

100

100

100

100

Genital aphthosis

82

31.6

70

83

55

58.3

88.2

Cutaneous signs

 

89.5

92

76

  

82.4

Erythema nodosum

52

36.8

40

37

22.7

44.2

26.5

Pseudo folliculitis

51

8/19

58

39

43

55.4

ND

Pathergy test +

37

41.2

-

45.5

NS

37.8

57.1

Ocular signs

35b

 

60

 

45

29.2

Approx 50 %

Anterior uveitis

47.4

 

31

30.1

47.1

Posterior uveitis

42.1

36

9 %

28

8.8

Retinal vasculitis

10.5

16.7

Arthralgia/arthritis

40

47.4

56

22

41

33.4

17.6

Gastro intestinal

4.8

36.8

14

NS

4.49

1.6

11.7

Neurologicala

7.2a

26.3

15

3.6a

5a

3a

5.8a

Vascular

9.6

10.5

15

3.6

15.38

4.4

26.5

Family history of BD

19

ND

15

12

24.4

ND

ND

Age first symptom (years)

12.3 (1–16)

6.9 ± 3.9

8.4 (0–16)

11.6 (1–16)

7.83 ± 4.39

ND

30.4 ± 8

  1. aOther than headaches buveitis without details + in this study patienst were classified by an international expert committee, independently of the international criteria