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Table 2 Pras et al. severity scoring system for pediatric FMF [11]

From: Relationship between clinical findings and genetic mutations in patients with familial Mediterranean fever

 

Variable

Score

Appearing of disease (year)

>11

2

6-10

3

<6

4

Frequency of attack on admission

<1

1

1-2

2

>2

3

Severity of arthritis

Acute

2

Degenerative

3

Erysipelas-like erythema

present

3

Required dosage of colchicine (mg/day)

<1

1

1-1.5

2

2

3

2a

4

  1. Note: Score 3-5 Mild; 6-8 moderate; >9 severe disease. anon-response to colchicine