Major criteria: |
1-Recurrent febrile episodes associated with peritonitis, pleuritis or synovitis |
2-Amyloidosis of AA-type without a predisposing disease |
3-Favorable response to daily colchicine |
Minor criteria: |
1-Recurrent febrile episodes |
2-Erysipelas-like erythema |
3-Positive history of familial Mediterranean fever in a first degree relative |
Definite Diagnosis: The diagnosis if definite is 2 major or 1 major + 2 minor criteria are met. |
Probable diagnosis: The diagnosis is probable if 1 major + 1 minor criterion are met. |