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Table 1 Tel-Hashomer diagnosis criteria [10]

From: Relationship between clinical findings and genetic mutations in patients with familial Mediterranean fever

Major criteria:

 1-Recurrent febrile episodes associated with peritonitis, pleuritis or synovitis

 2-Amyloidosis of AA-type without a predisposing disease

 3-Favorable response to daily colchicine

Minor criteria:

 1-Recurrent febrile episodes

 2-Erysipelas-like erythema

 3-Positive history of familial Mediterranean fever in a first degree relative

Definite Diagnosis: The diagnosis if definite is 2 major or 1 major + 2 minor criteria are met.

Probable diagnosis: The diagnosis is probable if 1 major + 1 minor criterion are met.