Total (n = 117) | JIA (n = 84) | SLE (n = 21) | Vasculitis (n = 6) | MCTD (n = 1) | Scleroderma/SLE overlap syndrome | |
---|---|---|---|---|---|---|
n (%) | n (%) | n (%) | n (%) | (n = 1) | ||
PIDs | 16 (13.7) | 6 (7.2) | 6 (28.6) | 2 (33.3)a | 1 | 1 |
C4D | 7 (6) | 3 (3.6) | 3 (14.3) | 1 (16.6) | 0 | 0 |
C2D | 3 (2.6) | 1 (1.2) | 2 (9.5) | 0 | 0 | 0 |
SIgAD | 5 (4.3) | 2 (2.4) | 1 (4.8) | 0 | 1 | 1 |
Unclassified hypogamma globulinaemia | 2 (1.7) | 0 | 0 | 2 (33.3) | 0 | 0 |