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Table 5 Revised Ghent criteria: systemic feature score (adapted from Faivre L et al. [38])

From: When flexibility is not necessarily a virtue: a review of hypermobility syndromes and chronic or recurrent musculoskeletal pain in children

Table 2: Revised Ghent Criteria: Systemic features score

• Wrist AND thumb sign – 3 (Wrist OR thumb sign – 1)

• Pectus carinatum deformity – 2 (pectus excavatum or chest asymmetry – 1)

• Hindfoot deformity – 2 (plain pes planus – 1)

• Pneumothorax – 2

• Dural ectasia – 2

• Protrusio acetabuli – 2

• Reduced US/LS AND increased arm/height AND no severe scoliosis – 1

• Scoliosis or thoracolumbar kyphosis– 1

• Reduced elbow extension – 1

• Facial features (3/5) – 1 (dolichocephaly, enophtalmos, downslanting palpebral fissures, malar hyoplasia, retrognathia)

• Skin striae – 1

• Mitral valve prolapse (all types) – 1

• Myopia >3 diopters – 1

Maximum total: 20 points; score ≥7 indicates systemic involvement

  1. Bold numbers refer to the points to be scored for each finding