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Table 1 Classification of Childhood Vasculitis by Özen et al.

From: Time to focus on outcome assessment tools for childhood vasculitis

Predominantly large-vessel vasculitis

Predominantly medium-sized vessel vasculitis

Predominantly small-vessel vasculitis

Other vasculitides

Takayasu arteritis

Childhood polyarteritis nodosa (c-PAN)

Granulomatous:

Wegener granulomatosis, Churg-Strauss syndrome

Behçet Disease

 

Cutaneous polyarteritis

Non-granulomatous:

Henoch-Scönlein purpura, Microspcopic polyangiitis, Hypocomplementemic urticarial vasculitis

Vasculitis secondary to infection (including Hep B associated PAN), malignancies and drugs, including hypersensitivity vasculitis

 

Kawasaki Disease

 

Vasculitis associated with connective tissue diseases

   

Isolated vasculitis of the central nervous system

   

Cogan syndrome

   

Unclassified