Author | Gender | Age | Symptoms | Oral/Genital ulcera | Myalgia | Conjunctivitis | Histology/angiography | Therapeutic regimen |
---|---|---|---|---|---|---|---|---|
Hughes [14] | m | 14 | PAA, CVST | nr | nr | nr | + | Â |
 | m | 14 | PAA, CVST, DVT | nr | nr | + | + | prednisolone |
Roberts [15] | m | 12 | PAA, DVT | nr | nr | nr | + | surgery |
Emad [7] | m | 16 | PAA, CVST, DVT | - | nr | - | + | prednisolone, azathioprin |
This report | m | 11 | PAA, CVST | - | + | - | + | cyclophosphamide prednisolone |