Pulmonary medium vessel vasculitis in an 11 year old boy: Hughes Stovin syndrome as a variant of polyarteritis nodosa?

Table 1 Pediatric cases of Hughes Stovin Syndrome

Author	Gender	Age	Symptoms	Oral/Genital ulcera	Myalgia	Conjunctivitis	Histology/angiography	Therapeutic regimen
Hughes [14]	m	14	PAA, CVST	nr	nr	nr	+
	m	14	PAA, CVST, DVT	nr	nr	+	+	prednisolone
Roberts [15]	m	12	PAA, DVT	nr	nr	nr	+	surgery
Emad [7]	m	16	PAA, CVST, DVT	-	nr	-	+	prednisolone, azathioprin
This report	m	11	PAA, CVST	-	+	-	+	cyclophosphamide prednisolone

m: male; PAA: pulmonary artery aneurysms; CVST: cerebral venous sinus thrombosis; DVT: deep venous thrombosis;
nr: not reported; + symptom present; - symptom absent.

ISSN: 1546-0096