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Table 2 Other reported autoinflammatory diseases

From: Periodic fever syndromes in Eastern and Central European countries: results of a pediatric multinational survey

Autoinflammatory disease

Reported

cases

PFAPA

282

Behçet disease

26

CRMO

23

Idiopathic recurrent pericarditis

2

Schnitzler syndrome

1

  1. PFAPA- periodic fever syndrome with aphthous stomatitis, pharyngitis and cervical adenopathy
  2. CRMO- chronic recurrent multifocal osteomyelitis