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Table 2 Post-transplant follow-up of patients

From: Farber disease: clinical presentation, pathogenesis and a new approach to treatment

Parameter

Patients

Patient number and gender

#1, female

#2, male

#3, female

#4, female

Patient origin

Muenster

Muenster

Muenster

Hamburg

Time point of follow-up

prior to SCT

day +450

prior to SCT

day +200

prior to SCT

day +270

prior to SCT

day +958

ESR (mm, first hour, Westergren)

38

9

53

12

25

13

no data available

Time point of follow-up

prior to SCT

day +1800

prior to SCT

day +1560

prior to SCT

day +990

prior to SCT

day +958

Number of nodules

58

0

39

0

18

0

pre Tx-nodules mainly dissolved, no new nodules

Number of joints with restricted mobility

26

0

24

0

10

0

almost all joints affected, however considerable improvement after HSCT

  1. Legend: The clinical evaluation of patients has been followed more closely, so laboratory data (i.e. ESR) are not available at each time-point of follow-up.