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Table 2 Post-transplant follow-up of patients

From: Farber disease: clinical presentation, pathogenesis and a new approach to treatment

Parameter Patients
Patient number and gender #1, female #2, male #3, female #4, female
Patient origin Muenster Muenster Muenster Hamburg
Time point of follow-up prior to SCT day +450 prior to SCT day +200 prior to SCT day +270 prior to SCT day +958
ESR (mm, first hour, Westergren) 38 9 53 12 25 13 no data available
Time point of follow-up prior to SCT day +1800 prior to SCT day +1560 prior to SCT day +990 prior to SCT day +958
Number of nodules 58 0 39 0 18 0 pre Tx-nodules mainly dissolved, no new nodules
Number of joints with restricted mobility 26 0 24 0 10 0 almost all joints affected, however considerable improvement after HSCT
  1. Legend: The clinical evaluation of patients has been followed more closely, so laboratory data (i.e. ESR) are not available at each time-point of follow-up.