Cardiopulmonary involvement in juvenile systemic sclerosis: development of recommendations for screening and investigation

Table 1 Recommendations for screening for cardiopulmonary involvement in JSSc at baseline and follow-up (75% consensus defined as agreement)

Cardiopulmonary	Baseline
	All patients should undergo: - BP - 12 lead ECG - 24 hour ECG - ECHO with Doppler - Cardiac MRI with gadolinium - HRCT thorax - PFT with DLCO - 6MWT
	Follow-up screening (for first 5 years from diagnosis)*
	6 monthly	12 lead ECG ECHO with doppler 6MWT PFT with DLCO
	Annual	24hr ECG
	At 3 years	Repeat HRCT

*screening guidelines are based on asymptomatic patients. However, children may need more frequent monitoring depending on clinical status and abnormalities detected on previous investigation.

ISSN: 1546-0096