Table 1
| Â | Fever and Urticarial Skin Rash (23 pts) | Periodic Fever (6 pts) | Urticarial Skin Rash (6 pts) |
|---|---|---|---|
Elevation of acute phase reactants | 22 | 4 | 2 |
Other Symptoms - Arthralgia -Transient arthritis - Conjunctivitis - Headache - Mental retardation - Dysmorphic bone | 22 9 7 9 1 1 | 2 0 1 2 0 1 | 3 2 1 1 0 0 |
Therapy - Steroids - NSAIDs - Anti IL-1 Blockers - Others | 13 15 6 10 | 3 3 0 0 | 5 3 1 3 |