| Diagnosis | Initial symptom | Age at onset, Gender | Observation period | Raynaud phenomenon | Sclerodactyly | Myositis | Organ involvement | CK(U/l)/ Ald(U/l) | ANA |
---|---|---|---|---|---|---|---|---|---|---|
clild onset | GM/PM | Multiple skin lesions | 7y Female | 8y6m | - | + | + | - | 1,249/ 20.9 | 1:1,280 |
adult onset | DM | Muscle weakness,Weight loss | 30y Female | 2y2m | + | - | + | IP | 4,699/ 53.8 | 1:2,560 |
 | SSc/PM | Muscle weakness, Joint pain | 32y Female | 12y0m | + | + | + | ED | 1,078/ 16.6 | 1:10,240 |
 | SSc/PM | Arthritis | 46y Female | 4y10m | + | + | + | IP,ED, Arthritis | 1,825/ 30.9 | 1:640 |