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Table 1 Demographics and disease characteristics

From: Clinical characteristics of children with juvenile dermatomyositis recruited within the first 7 months of the CARRAnet registry

Characteristc Number (%) of subjects   Characteristic Number (%) with characteristic ever Number (%) with characteristic at enrollment
Sex    Elevated muscle enzymes 86/89 (97%) 6/89 (7%)
Female 80 (78%)   Arthritis 34/86 (40%) 4/86 (5%)
Male 22 (22%)   Calcinosis 10/87 (12%) 7/87 (8%)
Ratio Female:male 3.6:1   Cardiac involvement 1/85 (1%) 1/85 (1%)
Race/Ethnicity    GI Ulceration 3/85 (4%) 1/85 (1%)
White, Non-Hispanic 65 (64%)   Dysphagia/Dysphonia 26/84 (31%) 1/84 (1%)
White, Hispanic 13 (13%)   ILD 1/84 (1%) 0/84 (0%)
African American 9 (9%)   Muscle weakness:   
American Indian 1 (1%)   None - 62/91 (68%)
Pacific Islander 1 (1%)   Mild - 23/91 (25%)
Multi-racial 10 (10%)   Moderate - 4/91 (4%)
Unknown 3 (3%)   Severe - 2/91 (2%)
1° Family hx of autoimmunity 21/92 (23%)   Periungual telangiectasia - 39/86 (45%)
Positive ANA 55/85 (65%)   Contractures - 7/91 (8%)
Chronology Median, yrs (quartiles) Range, yrs V or shawl sign - 5/91 (6%)
Age 10.6 (7.1, 14.8) 2.4-20.8 Lipodystrophy - 4/91 (4%)
Age of onset 6.0 (3.3, 9.5) 0.9-15.9 Skin ulcer - 3/91 (3%)
Disease duration 3.0 (1.7, 5.7) 0.2-12.8 Malar or facial erythema - 24/90 (27%)
Time to rhematologie care 0.32 (0.13, 0.67) 0-5.1 Gottron sign, papules, or heliotrope - 44/91 (48%)