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Table 7 Disease course response patterns

From: Is juvenile dermatomyositis a different disease in children up to three years of age at onset than in children above three years at onset? A retrospective review of 23 years of a single center’s experience

Disease course

Frequency in 3 years of age and below at onset n = 19

Frequency in above 3 years of age at onset n = 59

p-value

Monocyclic Disease

16 (84.2%)

20 (33.8%)

0.027

Polycyclic

1 (5.2%)

21 (35.5%)

0.019

Chronic continuous

2 (10.5%)

18 (30%)

0.03

Time in months from diagnosis to first remission

n = 13

n = 37

-

 

Mean = 23.62

Mean = 26.84

 
 

St Dev = 13.72

St Dev = 14.91

 
 

Median = 21

Median = 24

 
 

Range = 6 to 51

Range = 7 to 78

 
 

Mode = 6, 19

Mode = 23, 27

 

Duration in months of disease follow up

n = 19

n = 59

-

 

Mean = 78.4

Mean = 95.10

 
 

St Dev = 61.0

St Dev = 62.12

 
 

Median = 56.0

Median = 81

 
 

Range = 6 to 202

Range = 6 to 211

 
 

Mode = 36, 85

Mode = 21, 24, 26

 

Time in months to reach near normal muscle strength first time

n = 9

n = 41

-

 

Mean = 10.33

Mean = 8.29

 
 

St Dev = 10.37

St Dev = 10.53

 
 

Median = 6

Median = 6

 
 

Range = 5 to 37

Range = 1 to 62

 
 

Mode = 6

Mode = 6