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Table 1 Clinical and laboratory findings in SLE associated with prolidase deficiency

From: Prolidase deficiency associated with systemic lupus erythematosus (SLE): single site experience and literature review

Patient no (Reference) 1 Shrinath (19973) 2 Shrinath (19973) 3 Klar (2009) 4 Klar (2009) 5 Rocco (2007*4) 6 Bisonnette (19939) 7 Marotte (2010)1 8 Falik-Zaccai (201010) 9 Falik-Zaccai (201010) 10 Present report
Consanguinity + + + + ? ? unknown + + +
Ethnicity Pakistan Pakistan Arab Moslem Arab Moslem ? ? Portugal Druze Arab Moslem Druze
Sex M F F M M F M F F M
Age of PD/SLE diagnosis 9m/8y 6m/3y /8y /12y ? /16y /25y   5/8 2y/2.5
Skin involvement + + + + + + + + + +
Maculo-papular rash + + + - + + - + + +
Vasculitis + - - - + - Necrotic lesion - - +
Leg ulcers - - + + + + + - - -
Splenomegaly + - + + - - + + + +
Splenectomy - - - -   -   + - -
CNS involvement - - - - - - - _ + _
seizure          +  
Renal disease + - - - - + + - + +
Kidney biopsy - - -    Class III +   Class IV Kidney transplantation Class IV
Renal failure -   -    -     -
Hematological Disease + + +      + - +
Anemia/Leukopenia/thrombopenia + + +      + - +
Recurrent infections + + + + - +   + + -
Pulmonary disease + + + +   - + + + -
ANA + + + - + +   + + +
Positive ENA + + + + + + 1/640 + + +
Anti DNA + + + + + + - + + +
Hypocomplementemia + - - + + + + + + +
Fulfilled Criteria of SLE + + - - - + "Rhupus"2syndrome + + +