Table 2 Clinical features indicating active SJIA requiring initiation or increase of corticosteroids
On Line | Questionnaire | Face-to-Face Conference | ||
|---|---|---|---|---|
Consensus reached (%) | Increase cortico-steroids? | Consensus not reached | Consensus* | |
Increase corticosteroids in the presence of | ||||
Symptomatic pericarditis | Yes | Yes | Endorsed | |
Symptomatic myocarditis | Yes | Yes | Endorsed | |
Asymptomatic myocarditis (imaging only) | Yes | Yes | Endorsed | |
Symptomatic pleural effusion | Yes | Yes | Endorsed | |
Symptomatic pneumonitis | Yes | Yes | Endorsed | |
Fever for 6 of last 10 days | Yes | Yes | Changed to “No” | |
Fever for 8 of last 14 days | Yes | Yes | Changed to “No” | |
Anemia, Hgb <7 g/dl | Yes | Yes | Refined as “No” if ≥ 6.5 and asymptomatic | |
Anemia, Hgb 7–9 g/dl | X | No if ≥ 6.5 g/dl and symptomatic | ||
SJIA rash alone | Yes | No | Endorsed | |
Anorexia alone | Yes | No | Endorsed | |
Low albumin alone | Yes | No | Endorsed | |
Severe fatigue alone | X | No | ||
Weight loss alone | X | No | ||
Worsening synovitis* | Not evaluated | No | ||